E71 ICD 10 Code is a non-billable and non-specific code and should not be used to indicate a diagnosis for reimbursement purposes. There are other codes below it with greater level of diagnosis detail. The 2023 edition of the American ICD-10-CM code became effective on October 1, 2022.
Short description for E71 ICD 10 code:
Disord of branched-chain amino-acid metab & fatty-acid metab
Codes
- E71.0 Maple-syrup-urine disease
- E71.1 Other disorders of branched-chain amino-acid metabolism
- E71.11 Branched-chain organic acidurias
- E71.110 Isovaleric acidemia
- E71.111 3-methylglutaconic aciduria
- E71.118 Other branched-chain organic acidurias
- E71.12 Disorders of propionate metabolism
- E71.120 Methylmalonic acidemia
- E71.121 Propionic acidemia
- E71.128 Other disorders of propionate metabolism
- E71.19 Other disorders of branched-chain amino-acid metabolism
- E71.2 Disorder of branched-chain amino-acid metabolism, unspecified
- E71.3 Disorders of fatty-acid metabolism
- E71.30 Disorder of fatty-acid metabolism, unspecified
- E71.31 Disorders of fatty-acid oxidation
- E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency
- E71.311 Medium chain acyl CoA dehydrogenase deficiency
- E71.312 Short chain acyl CoA dehydrogenase deficiency
- E71.313 Glutaric aciduria type II
- E71.314 Muscle carnitine palmitoyltransferase deficiency
- E71.318 Other disorders of fatty-acid oxidation
- E71.32 Disorders of ketone metabolism
- E71.39 Other disorders of fatty-acid metabolism
- E71.4 Disorders of carnitine metabolism
- E71.40 Disorder of carnitine metabolism, unspecified
- E71.41 Primary carnitine deficiency
- E71.42 Carnitine deficiency due to inborn errors of metabolism
- E71.43 Iatrogenic carnitine deficiency
- E71.44 Other secondary carnitine deficiency
- E71.440 Ruvalcaba-Myhre-Smith syndrome
- E71.448 Other secondary carnitine deficiency
- E71.5 Peroxisomal disorders
- E71.50 Peroxisomal disorder, unspecified
- E71.51 Disorders of peroxisome biogenesis
- E71.510 Zellweger syndrome
- E71.511 Neonatal adrenoleukodystrophy
- E71.518 Other disorders of peroxisome biogenesis
- E71.52 X-linked adrenoleukodystrophy
- E71.520 Childhood cerebral X-linked adrenoleukodystrophy
- E71.521 Adolescent X-linked adrenoleukodystrophy
- E71.522 Adrenomyeloneuropathy
- E71.528 Other X-linked adrenoleukodystrophy
- E71.529 X-linked adrenoleukodystrophy, unspecified type
- E71.53 Other group 2 peroxisomal disorders
- E71.54 Other peroxisomal disorders
- E71.540 Rhizomelic chondrodysplasia punctata
- E71.541 Zellweger-like syndrome
- E71.542 Other group 3 peroxisomal disorders
- E71.548 Other peroxisomal disorders
Possible back-references that may be applicable or related to E71 ICD10 Code:
Present On Admission (POA Exempt)
E71 ICD 10 code is considered exempt from POA reporting
Clinical information about E71 ICD 10 code
Metabolism is the process your body uses to get or make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues, such as your liver, muscles, and body fat.
A metabolic disorder occurs when abnormal chemical reactions in your body disrupt this process. When this happens, you might have too much of some substances or too little of other ones that you need to stay healthy. There are different groups of disorders. Some affect the breakdown of amino acids, carbohydrates, or lipids. Another group, mitochondrial diseases, affects the parts of the cells that produce the energy.
You can develop a metabolic disorder when some organs, such as your liver or pancreas, become diseased or do not function normally. Diabetes is an example.
The information in this box was provided by MedlinePlus.gov